视神脊髓炎谱系疾病国际共识诊断.pdf

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PublishedAheadofPrintonJune19,2015as10.1212/WNL.0000000000001729VIEWS&REVIEWSInternationalconsensusdiagnosticcriteriaforneuromyelitisopticaspectrumdisordersDeanM.Wingerchuk,MD,FRCP(C)Neuromyelitisoptica(NMO)isaninfltoryCNSsyndromedisttfrommultiplesclerosisBrendaBanwell,MD,(MS)thatisassociatedwithserumaquaporin-4immunoglobulinGantibodies(AQP4-IgG).PriorFRCP(C)NMOdiagnosticcriteriarequiredopticnerveandspinalcordinvolvementbutmorerestrictedJeffreyL.Bet,MD,ormoreextensiveCNSinvolvementmayoccur.TheInternationalPanelforNMODiagnosis(IPND)PhDwasconvenedtodevelopreviseddiagnosticcriteriausingsystematieraturereviewsandelec-PhilippeCabre,MDtronicsurveystofacilitateconsensus.ThenewnomenclaturedefinestheunifyingtermNMOWilliamCarroll,MDspectrumdisorders(NMOSD),whichisstratifiedfurtherbyserologictest

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